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Journal of Oral & Dental Health(JODH)

ISSN: 2573-8224 | DOI: 10.33140/JODH

Impact Factor: 1.5

Recessive Dystrophic Epidermolysis Bullosa-Hallopeau-Siemens Subtype

Abstract

Alphy Alphonsa Sebastian and Hasan Subhi

Epidermolysis bullosa dystrophica is a mechanobullous disorder characterized by blister formation in response to minimal trauma. Dystrophic mechanism mainly affects the dermis below the lamina densa at the level of the anchoring fibrils. It is characterized by skin blisters contractures of digital web spaces, microstomia, and enamel hypoplasia and cementum disorders. The onset is in early childhood and heals with atrophic scars. This case features a 14 year old patient diagnosed with EBD with typical clinical features and histopathological findings

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