Pregnancy And Delivery in Late Diagnosed Kindler Syndrome: A Case Report And Review of The Literature

Abstract

Malihe Ghasemi, Mohammad Javad Najafi, Atousa Mortazavi Milani, Ghasem Rahmatpour Rokni and Amin Ghanbarpour

Epidermolysis bullosa is a collection of infrequent, diverse, and genetic disorders with four primary classifications, identified by the skin’s vulnerability and, in some cases, mucosal fragility. The skin and mucosal layers separate when subjected to friction or mechanical stress, leading to blisters and erosions within these tissues. A woman aged 29, afflicted with Kindler syndrome, presented at our hospital experiencing labor contractions. Her skin condition remained unaltered throughout her pregnancy and post-childbirth period. A cesarean section was carried out at the 38-week gestation mark due to an unplanned membrane rupture and dense meconium presence. The healing of the surgical wound proceeded without complications. In this instance, the patient’s pregnancy did not intensify the skin-related symptoms of Kindler syndrome. It is critical to manage perioperative care to safeguard susceptible skin and mucosa carefully. The patient’s journey throughout pregnancy and the postnatal period proceeded without notable incidents. Individuals with EB giving birth often require substantial assistance due to their condition.

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