Arthrogryposis and Veptr: One Centre Case Series

Abstract

Maredi E, Vommaro F, Giacomini S, Scarale A, Baioni A, Di SilvestreM, Pipola V, Pescuma G and Greggi T

As in others rare syndromes Kyphoscoliosis is the most common deformity you can find, and is a very early onset, rapidly evolving and become very stiff from early age. The incidence of scoliosis in arthrogryposis in literature varies from 30% to 67%. Due to the complexity of the clinical is necessary a multidisciplinary approach and as soon as possible (Pediatric orthopedic surgeon, anesthesiologist, pulmonologist). There are a limited number of studies on arthrogryposis and early onset scoliosis (EOS) surgically treated. We reviewed our children affected by EOS in arthrogryposis and surgically treated to describe the efficacy or ribbased distraction systems in these particular cases of deformities. We use Vertical Expandable Prosthetic Titanium Rib (VEPTR1 and 2) device.

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