A systematic review was conducted using MEDLINE using the terms “atypical teratoid rhabdoid tumor” AND “adult.” The systematic review was supplemented with relevant articles from the references. Cases were included if the pathology was confirmed by loss of INI1 or BRG1. We included a case from our institution. The dataset was analyzed using descriptive statistics and log-rank test.

Primary rhabdoid tumor of lung is a rare histological and clinical entity. Lung tumors with rhabdoid features have been included as variants of large-cell carcinoma in the 1999 World Health Organization (WHO) classification of lung tumors. A large-cell carcinoma with a rhabdoid phenotype (LCCRP) is unusual, with only 38 cases reported till date. We report the clinical details of one such case that was treated with pneumonectomy and adjuvant chemotherapy. We also present a review of the literature.

Endometrial carcinoma (EC) and ovarian carcinoma (OvCa) are two common female cancers, accounting for 4th and 5th-leading causes of cancer death among women in the United States (Siegel, Miller & Jemal, 2019). EC can be divided into two subgroups, a type I endometrioid tumors and a type II serous-like tumor (Getz et al., 2013). Compared to type I EC, type II serous-like EC was characterized with a more advanced stage and worse outcome.