Inborn errors of super molecule metabolism coated during this chapter embody enzyme deficiencies, disorders of monosaccharide metabolism, polysome storage diseases, and gluconeogenic disorders. This focuses principally on clinical aspects, biological science and current treatments for these disorders. The defective digestion of dietary disaccharides starch, milk sugar and saccharose is thanks to deficiencies of innate Lactaid, adult-type Lactaid, or sucrase-isomaltose. Disorders of monosaccharide metabolism embody defects in transport enzymes of saccharose metabolism enzymes of fruit sugar metabolism To date, there are over twelve glycogenosis, or polysome metabolism disorders, that are cataloged. polysome storage diseases (GSD), a significant class of glycogenosis, are classified by the kind of tissue involved: liver, muscle, and/or internal organ. Gluconeogenic disorders entail deficiencies of fructose-1,6-diphosphatase, pyruvate carboxylase, phosphoenolpyruvate carboxin’s, and pyruvate dehydrogenase advanced. Metabolism is that the method your body uses to form energy from the food you eat. Food is created from proteins, carbohydrates, and fats. Chemicals in your gastrointestinal system break the food components down into sugars and acids, your body's fuel.